Medicines
- Buphenyl sodium phenylbutyrate · Generic available High blood ammonia from a urea cycle disorder
- Ravicti glycerol phenylbutyrate · Generic available Urea cycle disorders (UCDs)
- Ammonul sodium benzoate and sodium phenylacetate · Generic available High blood ammonia from a urea cycle disorder
- Carbaglu carglumic acid · Generic available High blood ammonia from NAGS deficiency
- Loargys pegzilarginase-nbln · No generic yet High blood arginine from arginase 1 deficiency (ARG1-D)
- Olpruva sodium phenylbutyrate · No generic yet
- Pheburane sodium phenylbutyrate · No generic yet
From each medicine’s FDA label. Only your prescriber can say which one is right for you, and many are prescribed for other reasons too.